Erdheim-chester disease associated with marginal zone lymphoma and monoclonal proteinemia.

Academic Article


  • Erdheim-Chester disease (ECD) is a rare non-Langerhans cell histiocytosis. We report a fatal case of ECD with extensive cardiac involvement associated with a marginal zone lymphoma and monoclonal proteinemia in a young man. This is the first reported association of ECD with a monoclonal gammopathy or a lymphoma.
  • Published In

    Digital Object Identifier (doi)

    Author List

  • Pavlidakey PG; Mohanty A; Kohler LJ; Meyerson HJ
  • Start Page

  • 941637
  • Volume

  • 2011