Assessing the prevalence of juvenile systemic sclerosis in childhood using administrative claims data from the United States

Academic Article


  • Juvenile systemic sclerosis is a very rare orphan disease. To date, only one publication has estimated the prevalence of juvenile systemic sclerosis using a survey of specialized physicians. We conducted a study of administrative claims data in the United States using the International Classification of Diseases, Ninth Revision diagnosis codes and found a prevalence of approximately 3 per 1,000,000 children. This estimate will inform the planning of prospective studies.
  • Digital Object Identifier (doi)

    Author List

  • Beukelman T; Xie F; Foeldvari I
  • Start Page

  • 189
  • End Page

  • 190
  • Volume

  • 3
  • Issue

  • 2