Aortopulmonary Septal Defect

Academic Article


  • An aortopulmonary (AP) septal defect, also known as an AP window, is one of the rarest congenital heart defects accounting for less than 0.5% of forms of congenital heart disease.[1] This defect can occur in isolation or concurrently with other forms of congenital heart disease such as a ventricular septal defect, interruption of the aortic arch, tetralogy of Fallot, and very rarely, coronary artery anomalies.[2][3][4][5][6] By definition, the AP window is a direct "side to side" connection of the ascending aorta to the main pulmonary artery but with the formation of a normal aortic valve and a right ventricular outflow tract, differentiating it from truncus arteriosus.[7] Embryologically an AP window develops when there is incomplete septation of the great arteries.
  • Authors

    Author List

  • Law MA; Mahajan K