Renal angiomyolipoma associated with lymph node involvement and renal cell carcinoma in patients with tuberous sclerosis

Academic Article


  • Renal angiomyolipomas are found in more than half of the patients with tuberous sclerosis. We report on 3 patients with tuberous sclerosis and pathologically aggressive renal angiomyolipoma with retroperitoneal lymph node involvement and/or renal cell carcinoma. All patients have had a benign course. The literature is reviewed and supports the benign nature of this seemingly aggressive disorder. An approach to the evaluation and treatment of a child with tuberous sclerosis and renal angiomyolipoma is presented.
  • Digital Object Identifier (doi)

    Author List

  • Taylor RS; Joseph DB; Kohaut EC; Wilson ER; Bueschen AJ
  • Start Page

  • 930
  • End Page

  • 932
  • Volume

  • 141
  • Issue

  • 4 I