Positions

Selected Publications

Academic Article

Year Title Altmetric
2022 Ivacaftor-elexacaftor-tezacaftor and tacrolimus combination in cystic fibrosisJournal of Cystic Fibrosis.  21:e8-e10. 2022
2022 Use of elexacaftor/tezacaftor/ivacaftor among cystic fibrosis lung transplant recipientsJournal of Cystic Fibrosis2022
2021 CFTR function and clinical response to modulators parallel nasal epithelial organoid swellingAmerican Journal of Physiology: Lung Cellular and Molecular Physiology.  321:L119-L129. 2021
2021 Combination CFTR modulator therapy in children and adults with cystic fibrosisThe Lancet Respiratory Medicine.  9:677-679. 2021
2021 Long term clinical effectiveness of ivacaftor in people with the G551D CFTR mutationJournal of Cystic Fibrosis.  20:213-219. 2021
2020 Highlights from the 2019 North American Cystic Fibrosis ConferencePediatric Pulmonology.  55:2225-2232. 2020
2020 Variable cellular ivacaftor concentrations in people with cystic fibrosis on modulator therapyJournal of Cystic Fibrosis.  19:742-745. 2020
2020 Human nasal epithelial organoids for therapeutic development in cystic fibrosisGenes.  11:1-17. 2020
2020 Females with cystic fibrosis demonstrate a differential response profile to ivacaftor compared with malesAmerican Journal of Respiratory and Critical Care Medicine.  201:996-998. 2020
2019 Co-cultured microfluidic model of the airway optimized for microscopy and micro-optical coherence tomography imagingBiomedical Optics Express.  10:5414-5430. 2019
2019 Effectiveness of ivacaftor in cystic fibrosis patients with non-G551D gating mutationsJournal of Cystic Fibrosis.  18:102-109. 2019
2018 Tracheostomy in children: Epidemiology and clinical outcomesPediatric Pulmonology.  53:1269-1275. 2018
2018 Potential pathogenicity of Inquilinus limosus in a pediatric patient with cystic fibrosisPediatric Pulmonology.  53:E21-E23. 2018
2018 Sensitivity of ivacaftor to drug-drug interactions with rifampin, a cytochrome P450 3A4 inducerPediatric Pulmonology.  53:E6-E8. 2018
2017 Nasospheroids permit measurements of CFTR-dependent fluid transportJCI insight.  2. 2017
2017 Toward inclusive therapy with CFTR modulators: Progress and challengesPediatric Pulmonology.  52:S4-S14. 2017
2009 Correlation of microRNA levels during hypoxia with predicted target mRNAs through genome-wide microarray analysisBMC Medical Genomics.  2. 2009
2008 Role of oxygen availability in CFTR expression and functionAmerican Journal of Respiratory Cell and Molecular Biology.  39:514-521. 2008
2004 Efficient intracellular processing of the endogenous cystic fibrosis transmembrane conductance regulator in epithelial cell linesJournal of Biological Chemistry.  279:22578-22584. 2004
2003 EWS/FLI function varies in different cellular backgroundsExperimental Cell Research.  290:414-419. 2003
2001 Peptides, made to orderScientist (Philadelphia, Pa.).  15:25-26. 2001
2001 Tailored arraysScientist (Philadelphia, Pa.).  15:26-28. 2001

Full Name

  • Jennifer Guimbellot