Selected Publications

Academic Article

Year Title Altmetric
2019 Spinal Cord Diffuse Midline Glioma in a 4-Year-Old Boy.Child Neurology Open.  6:2329048X19842451. 2019
2018 Cannabidiol improves frequency and severity of seizures and reduces adverse events in an open-label add-on prospective studyEpilepsy and Behavior.  87:131-136. 2018
2018 Cannabidiol improves frequency and severity of seizures and reduces adverse events in an open-label add-on prospective study Pongkiat Kankirawatana, Dr Rani Singh, Professor David G Standaert, Dr Yuliang Liu, Dr Leon Dure, Dr Jennifer DeWollfe, Professor Gary Cutter, Dr Tyler Gaston, Dr Ashley Thomas, Professor E. Martina Bebin, Dr. Lawrence Ver HoefEpilepsy and Behavior.  (in press). 2018
2014 UBQLN2 mutation causing heterogeneous X-linked dominant neurodegenerationAnnals of Neurology.  75:793-798. 2014
2013 Methodology of clinical research in rare diseases: Development of a research program in juvenile neuronal ceroid lipofuscinosis (JNCL) via creation of a patient registry and collaboration with patient advocatesContemporary Clinical Trials.  35:48-54. 2013
2013 Comprehensive behavioral intervention to improve occupational performance in children with tourette disorderAmerican Journal of Occupational Therapy.  67:194-200. 2013
2012 Pathologic features of dilated cardiomyopathy with localized noncompaction in a child with deletion 1p36 syndromeCongenital Heart Disease.  7:59-61. 2012
2009 Optimal clinical management of children receiving the ketogenic diet: Recommendations of the International Ketogenic Diet Study GroupEpilepsia.  50:304-317. 2009
2008 Randomized controlled trial of ethyl-eicosapentaenoic acid in huntington diseaseArchives of Neurology.  65:1582-1589. 2008
2007 The relationship between CAG repeat length and age of onset differs for Huntington's disease patients with juvenile onset or adult onsetAnnals of Human Genetics.  71:295-301. 2007
2006 Standardized assessment of behavior and adaptive living skills in juvenile neuronal ceroid lipofuscinosisDevelopmental Medicine and Child Neurology.  48:259-264. 2006
2005 Regarding "Antibiotic prophylaxis with azithromycin or penicillin for childhood-onset neuropsychiatric disorders" (multiple letters)Biological Psychiatry.  58:916-919. 2005
2005 Regarding "antibiotic prophylaxis with azithromycin or penicillin for childhood-onset neuropsychiatric disorders".Biological Psychiatry.  58. 2005
2003 Paroxysmal Dyskinesias in Children.Current Treatment Options in Neurology.  5:275-278. 2003
2000 Mammal-like striatal functions in Anolis. II. Distribution of dopamine D1 and D2 receptors, and a laminar pattern of basal ganglia sub-systemsBrain, Behavior and Evolution.  56:249-258. 2000
1997 Ectopically expressed CAG repeats cause intranuclear inclusions and a progressive late onset neurological phenotype in the mouseCell.  91:753-763. 1997
1997 Is cell death necessary for hippocampal mossy fiber sprouting?Epilepsy Research.  27:67-76. 1997
1997 Tourette syndromeCurrent Opinion in Neurology.  10:153-159. 1997
1995 DNA fragmentation and immediate early gene expression in rat striatum following quinolinic acid administrationExperimental Neurology.  133:207-214. 1995
1995 Huntington's disease gene: Regional and cellular expression in brain of normal and affected individualsAnnals of Neurology.  37:218-230. 1995
1994 IT15 gene expression in fetal human brainBrain Research.  659:33-41. 1994
1992 Preferential loss of striato‐external pallidal projection neurons in presymptomatic Huntington's diseaseAnnals of Neurology.  31:425-430. 1992
1991 Excitatory amino acid binding sites in the caudate nucleus and frontal cortex of huntington's diseaseAnnals of Neurology.  30:785-793. 1991
1991 Excitatory amino acidergic pathways and receptors in the basal gangliaAmino Acids.  1:339-350. 1991
1988 Childhood-onset movement disordersCurrent opinion in neurology and neurosurgery.  1:347-352. 1988
1985 Ribavirin small-particle aerosol treatment of infections caused by influenza virus strains A/Victoria/7/83 (H1N1) and B/Texas/1/84Antimicrobial Agents and Chemotherapy.  27:309-313. 1985


Year Title Altmetric
2020 A Multidisciplinary Clinic for the Management of Chiari I Malformations.  599-603. 2020
2013 A multidisciplinary clinic for the management of Chiari i malformations.  345-350. 2013
2006 Movement disorders in childhood 2006
2006 Treatment of Tics 2006
2005 Tremor in childhood.  145-149. 2005
2004 The treatment of comorbid attention-deficit disorder and Tourette's syndrome.  455-465. 2004
2002 DOPA-responsive dystonia 2002
2002 Paroxysmal movement disorders in childhood.  379-382. 2002
2000 Tourette syndrome and other tic disorders.  324-325. 2000
1999 Huntington's Disease.  90-91. 1999
1999 Sydenham's chorea.  216-217. 1999
1998 Neuropsychological Aspects of Movement Disorders in Children.  961-976. 1998
1996 Seizures and epilepsy.  613-624. 1996
1995 The distribution of glutamate receptor subtypes in mammalian central nervous system using quantitative in vitro autoradiography.  400-400. 1995
1992 Excitatory amino acid binding sites in the basal ganglia, primary visual cortex, and spinal cord.  179-188. 1992
1992 Excitatory amino acids in Huntington's disease.  217-222. 1992

Education And Training

  • Babies Hospital, Columbia Presbyterian Medical Center Pediatrics, Residency
  • Baylor College of Medicine Division of Pediatric Neurology, Department of Pediatrics, Residency
  • Columbia Presbyterian Medical Center, Residency
  • Baylor College of Medicine, Postdoctoral Fellowship
  • University of Michigan Hospitals & Health Centers, Postdoctoral Fellowship
  • University of Michigan Neurology, Postdoctoral Fellowship
  • University of Michigan Neurology, Postdoctoral Fellowship
  • Doctor of Medicine, Baylor College of Medicine 1984
  • Full Name

  • Leon Dure