Year |
Title |
Altmetric |
2021
|
LPS decreases CFTR open probability and mucociliary transport through generation of reactive oxygen species.
Redox Biology.
43.
2021
|
|
2017
|
miR-200b downregulates CFTR during hypoxia in human lung epithelial cells
2017
|
|
2017
|
Influenza virus infection alters ion channel function of airway and alveolar cells: Mechanisms and physiological sequelae
2017
|
|
2016
|
Limited ATF4 expression in degenerating retinas with ongoing ER stress promotes photoreceptor survival in a mouse model of autosomal dominant retinitis pigmentosa.
PLoS ONE.
11.
2016
|
|
2016
|
Mechanistic Approaches to Improve Correction of the Most Common Disease-Causing Mutation in Cystic Fibrosis.
PLoS ONE.
11.
2016
|
|
2016
|
A synonymous codon change alters the drug sensitivity of ΔF508 cystic fibrosis transmembrane conductance regulator.
The FASEB Journal.
30:201-213.
2016
|
|
2015
|
Decoding mechanisms by which silent codon changes influence protein biogenesis and function
2015
|
|
2015
|
Influenza virus M2 targets cystic fibrosis transmembrane conductance regulator for lysosomal degradation during viral infection.
The FASEB Journal.
29:2712-2725.
2015
|
|
2015
|
▵F508 CFTR surface stability is regulated by DAB2 and CHIP-mediated ubiquitination in post-endocytic compartments.
PLoS ONE.
10.
2015
|
|
2013
|
The silent codon change I507-ATC→ATT contributes to the severity of the AF508 CFTR channel dysfunction.
The FASEB Journal.
27:4630-4645.
2013
|
|
2013
|
Cigarette smoke and CFTR: Implications in the pathogenesis of COPD
2013
|
|
2013
|
Regulation of angiogenesis by hypoxia: The role of microRNA
2013
|
|
2012
|
The CFTR and ENaC debate: How important is ENaC in CF lung disease?
2012
|
|
2012
|
Glioma-specific cation conductance regulates migration and cell cycle progression.
Journal of Biological Chemistry.
287:4053-4065.
2012
|
|
2012
|
Dab2 is a key regulator of endocytosis and post-endocytic trafficking of the cystic fibrosis transmembrane conductance regulator.
Biochemical Journal.
441:633-643.
2012
|
|
2011
|
The Unfolded Protein Response (UPR)-activated transcription factor X-box-binding protein 1 (XBP1) induces microRNA-346 expression that targets the human antigen peptide transporter 1 (TAP1) mRNA and governs immune regulatory genes.
Journal of Biological Chemistry.
286:41862-41870.
2011
|
|
2011
|
Suppression of CFTR premature termination codons and rescue of CFTR protein and function by the synthetic aminoglycoside NB54
2011
|
|
2011
|
Interaction of ASIC1 and ENaC subunits in human glioma cells and rat astrocytes
2011
|
|
2011
|
CFTR expression regulation by the unfolded protein response.
Methods in Enzymology.
491:3-24.
2011
|
|
2010
|
A synonymous single nucleotide polymorphism in ΔF508 CFTR alters the secondary structure of the mRNA and the expression of the mutant protein.
Journal of Biological Chemistry.
285:28741-28748.
2010
|
|
2010
|
Targets for cystic fibrosis therapy: Proteomic analysis and correction of mutant cystic fibrosis transmembrane conductance regulator.
Expert Review of Proteomics.
7:495-506.
2010
|
|
2010
|
Functional stability of rescued ΔF508 cystic fibrosis transmembrane conductance regulator in airway epithelial cells.
American Journal of Respiratory Cell and Molecular Biology.
42:363-372.
2010
|
|
2009
|
Knockdown of ASIC1 and epithelial sodium channel subunits inhibits glioblastoma whole cell current and cell migration.
Journal of Biological Chemistry.
284:24526-24541.
2009
|
|
2009
|
Search and rescue finding ways to correct ΔF508 CFTR.
American Journal of Respiratory Cell and Molecular Biology.
40:385-387.
2009
|
|
2008
|
Activation of the unfolded protein response by ΔF508 CFTR.
American Journal of Respiratory Cell and Molecular Biology.
39:448-457.
2008
|
|
2008
|
Activation of the unfolded protein response by F508 cystic fibrosis transmembrane conductance regulator.
American Journal of Respiratory Cell and Molecular Biology.
39:448-457.
2008
|
|
2008
|
Somatic mosaicism for copy number variation in differentiated human tissues.
Human Mutation.
29:1118-1124.
2008
|
|
2008
|
The mechanism of cystic fibrosis transmembrane conductance regulator transcriptional repression during the unfolded protein response.
Journal of Biological Chemistry.
283:12154-12165.
2008
|
|
2008
|
Enhanced cell-surface stability of rescued ΔF508 cystic fibrosis transmembrane conductance regulator (CFTR) by pharmacological chaperones.
Biochemical Journal.
410:555-564.
2008
|
|
2007
|
Bioelectric effects of quinine on polarized airway epithelial cells.
Journal of Cystic Fibrosis.
6:351-359.
2007
|
|
2007
|
Restoration of W1282X CFTR activity by enhanced expression.
American Journal of Respiratory Cell and Molecular Biology.
37:347-356.
2007
|
|
2007
|
No detectable improvements in cystic fibrosis transmembrane conductance regulator by nasal aminoglycosides in patients with cystic fibrosis with stop mutations.
American Journal of Respiratory Cell and Molecular Biology.
37:57-66.
2007
|
|
2007
|
VCP/p97 AAA-ATPase does not interact with the endogenous wild-type cystic fibrosis transmembrane conductance regulator.
American Journal of Respiratory Cell and Molecular Biology.
36:706-714.
2007
|
|
2007
|
Endoplasmic reticulum stress and the unfolded protein response regulate genomic cystic fibrosis transmembrane conductance regulator expression
2007
|
|
2006
|
Mutations in the amino terminus of the cystic fibrosis transmembrane conductance regulator enhance endocytosis.
Journal of Biological Chemistry.
281:3329-3334.
2006
|
|
2005
|
Failure of cAMP agonists to activate rescued ΔF508 CFTR in CFBE41o- airway epithelial monolayers
2005
|
|
2005
|
Failure of Physiological Wild Type CFTR Stimulants to Activate Rescued ∆F508 CFTR in Airway Epithelial Monolayers
2005
|
|
2005
|
Establishment and characterization of a novel polarized MDCK epithelial cellular model for CFTR studies.
Cellular Physiology and Biochemistry.
16:281-290.
2005
|
|
2005
|
Consequences of C-terminal domains and N-terminal signal peptide deletions on LEKTI secretion, stability, and subcellular distribution.
Archives of Biochemistry and Biophysics.
435:89-102.
2005
|
|
2004
|
Excellent in vivo bystander activity of fludarabine phosphate against human glioma xenografts that express the Escherichia coli purine nucleoside phosphorylase gene.
Cancer Research.
64:6610-6615.
2004
|
|
2004
|
Assessment of CFTR localisation in native airway epithelial cells obtained by nasal brushing.
Journal of Cystic Fibrosis.
3:43-48.
2004
|
|
2004
|
Efficient intracellular processing of the endogenous cystic fibrosis transmembrane conductance regulator in epithelial cell lines.
Journal of Biological Chemistry.
279:22578-22584.
2004
|
|
2004
|
Extracellular Zinc and ATP Restore Chloride Secretion across Cystic Fibrosis Airway Epithelia by Triggering Calcium Entry.
Journal of Biological Chemistry.
279:10720-10729.
2004
|
|
2004
|
Gene delivery systems - Gene therapy vectors for cystic fibrosis.
Journal of Cystic Fibrosis.
3:203-212.
2004
|
|
2003
|
Gentamicin-induced correction of CFTR, function in patients with cystic fibrosis and CFTR stop mutations.
New England Journal of Medicine.
349:1433-1441.
2003
|
|
2003
|
Transient transfection of polarized epithelial monolayers with CFTR and reporter genes using efficacious lipids
2003
|
|
2003
|
Transient transfection of polarized epithelial monolayers with CFTR and reporter genes using efficacious lipids.
2003
|
|
2003
|
Protein Trafficking in the Endocytic Pathway: Studies on the Transferrin Receptor and the Cystic Fibrosis Transmembrane Conductance Regulator.
Recent Research Developments in Cell Research.
1:203-216.
2003
|
|
2002
|
Ablation of internalization signals in the carboxyl-terminal tail of the cystic fibrosis transmembrane conductance regulator enhances cell surface expression.
Journal of Biological Chemistry.
277:49952-49957.
2002
|
|
2002
|
Reactive oxygen nitrogen species decrease cystic fibrosis transmembrane conductance regulator expression and cAMP-mediated Cl- secretion in airway epithelia.
Journal of Biological Chemistry.
277:43041-43049.
2002
|
|
2002
|
Aminoglycoside suppression of a premature stop mutation in a Cftr-/- mouse carrying a human CFTR-G542X transgene
2002
|
|
2002
|
Novel regulation of cell [Na(+)] in macula densa cells: apical Na(+) recycling by H-K-ATPase.
2002
|
|
2002
|
Novel regulation of cell [Na+] in macula densa cells: Apical Na+ recycling by H-K-ATPase
2002
|
|
2001
|
A clinical inflammatory syndrome attributable to aerosolized lipid-DNA administration in cystic fibrosis.
Human Gene Therapy.
12:751-761.
2001
|
|
2001
|
Evidence that systemic gentamicin suppresses premature stop mutations in patients with cystic fibrosis.
American Journal of Respiratory and Critical Care Medicine.
163:1683-1692.
2001
|
|
2001
|
Improved oxygenation promotes CFTR maturation and trafficking in MDCK monolayers
2001
|
|
2001
|
Improved oxygenation promotes CFTR maturation and trafficking in MDCK monolayers.
2001
|
|
2000
|
Macula densa Na+/H+ exchange activities mediated by apical NHE2 and basolateral NHE4 isoforms
2000
|
|
2000
|
Macula densa Na+/H+ exchange activities mediated by apical NHE2 and basolateral NHE4 isoforms
2000
|
|
1999
|
CFTR involvement in chloride, bicarbonate, and liquid secretion by airway submucosal glands..
American Journal of Physiology.
277:L694-L699.
1999
|
|
1999
|
Characterization and dynamics of aggresome formation by a cytosolic GFP- chimera
1999
|
|
1999
|
CFTR involvement in chloride, bicarbonate, and liquid secretion by airway submucosal glands
1999
|
|
1998
|
The mechanism underlying cystic fibrosis transmembrane conductance regulator transport from the endoplasmic reticulum to the proteasome includes Sec61β and a cytosolic, deglycosylated intermediary.
Journal of Biological Chemistry.
273:29873-29878.
1998
|
|
1998
|
Cystic fibrosis transmembrane conductance regulator (CFTR) nucleotide- binding domain 1 (NBD-1) and CFTR truncated within NBD-1 target to the epithelial plasma membrane and increase anion permeability.
Biochemistry.
37:15222-15230.
1998
|
|
1998
|
Early events in CFTR biogenesis and degradation.
The FASEB Journal.
12.
1998
|
|
1998
|
Activation of ΔF508 CFTR in an epithelial monolayer
1998
|
|
1997
|
Purification, characterization, and expression of CFTR nucleotide- binding domains.
Journal of Bioenergetics and Biomembranes.
29:475-482.
1997
|
|
1997
|
Suppression of a CFTR premature stop mutation in a bronchial epithelial cell line.
Nature Medicine.
3:1280-1284.
1997
|
|
1996
|
Efficiency of plasmid delivery and expression after lipid-mediated gene transfer to human cells in vitro.
Journal of Pharmacology and Experimental Therapeutics.
279:1462-1469.
1996
|
|
1996
|
A method for the rapid detection of recombinant CFTR during gene therapy in cystic fibrosis
1996
|
|
1996
|
Development of drug targeting based on recombinant expression of the chicken avidin gene.
Journal of Drug Targeting.
4:41-49.
1996
|
|
1995
|
Cationic lipids for reporter gene and CFTR transfer to rat pulmonary epithelium
1995
|
|
1995
|
Bystander Killing of Melanoma Cells Using the Human Tyrosinase Promoter to Express the Escherichia coli Purine Nucleoside Phosphorylase Gene.
Cancer Research.
55:3339-3345.
1995
|
|
1995
|
Severe phenotype in mice with termination mutation in exon 2 of cystic fibrosis gene.
Somatic Cell and Molecular Genetics.
21:177-187.
1995
|
|
1995
|
Cationic lipids for reporter gene and CFTR transfer to rat pulmonary epithelium.
1995
|
|
1994
|
Informed consent to participate in a research study.
Human Gene Therapy.
5:1271-1277.
1994
|
|
1994
|
Tumor cell bystander killing in colonic carcinoma utilizing the Escherichia coli DeoD gene to generate toxic purines
1994
|
|
1994
|
Gene Therapy for Cystic Fibrosis Using Cationic Liposome Mediated Gene Transfer: A Phase I Trial of Safety and Efficacy in the Nasal Airway..
Human Gene Therapy.
5:1259-1277.
1994
|
|
1994
|
Informed consent to participate in a research study -- gene therapy for cystic fibrosis using cationic liposome mediated gene transfer: a phase I trial of safety and efficacy in the nasal airway..
Human Gene Therapy.
5:1271-1277.
1994
|
|
1994
|
Prognostic relevance of transforming growth factor alpha (TGF-α) and tumor necrosis factor alpha (TNF-α) detected in breast cancer tissues by immunohistochemistry.
Breast Cancer Research and Treatment.
29:229-235.
1994
|
|
1993
|
Creation of monoclonal antibodies against tumor necrosis factor-alpha (TNF-alpha) and transforming growth factor alpha (TFG-alpha), their definition and possible use
1993
|
|
1992
|
Cellular enzyme-linked immunocircle assay. A rapid assay of hybridomas produced against cell surface antigens.
Journal of Immunological Methods.
153:141-149.
1992
|
|
1991
|
Long-term effect of immunization with neural and nonneural antigens on the noradrenaline and serotonin levels of discrete brain areas in mice and the relationship between neurotransmitter levels and antibody production..
Acta Physiologica Hungarica.
77:85-92.
1991
|
|
1988
|
Oligopeptides and phagocytosis in mice..
Acta paediatrica Academiae Scientiarum Hungaricae.
29:45-48.
1988
|
|